| CASE REPORT |
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| Year : 2013 | Volume
: 79
| Issue : 1 | Page : 83--87 |
Familial leiomyomatosis cutis affecting nine family members in two successive generations including four cases of Reed's syndrome
Rajesh Kumar Mandal1, Sankha Koley1, Sabyasachi Banerjee1, Sankar Prasad Kabiraj2, Sudip Kumar Ghosh3, Piyush Kumar4
1 Department of Dermatology, Venereology, and Leprosy, North Bengal Medical College, Darjeeling, West Bengal, India
2 Department of Radiology, North Bengal Medical College, Darjeeling, West Bengal, India
3 Department of Dermatology, Venereology, and Leprosy, R. G. Kar Medical College, Kolkata, West Bengal, India
4 Department of Dermatology, Venereology, and Leprosy, Katihar Medical College, Katihar, Bihar, India
Correspondence Address:
Rajesh Kumar Mandal
Department of Dermatology, Venereology, and Leprosy, North Bengal Medical College, Darjeeling, West Bengal
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/0378-6323.104674
Reed's syndrome or familial leiomyomatosis cutis et uteri is an autosomal dominant disorder, characterized by multiple cutaneous and uterine leiomyomas. We report here a case of a 53-year-old woman who presented to us with multiple painful nodules over different parts of her body. Based on the histopathological examination, imaging, and past medical records, a diagnosis of Reed's syndrome was made. Three of her sisters had similar disease. Subsequently, it was found that a total of nine members of their family in two successive generations were affected with cutaneous leiomyomas. The present case series has been reported for its interesting clinical presentations and rarity.
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