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Year : 2019  |  Volume : 85  |  Issue : 5  |  Page : 481-485

Hemophagocytic lymphohistiocytosis: A rare, potentially fatal complication in subcutaneous panniculitis like T cell lymphoma

Chandra Sekhar Sirka1, Swetalina Pradhan1, Susama Patra2, Somanath Padhi2, Saroj Kumar DasMajumdar3, Debjani Panda1 
1 Department of Dermatology, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
2 Department of Pathology, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
3 Department of Radiotherapy, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India

Correspondence Address:
Dr. Chandra Sekhar Sirka
Department of Dermatology, All India Institute of Medical Sciences, Bhubaneswar, Odisha
India

Subcutaneous panniculitis-like T cell lymphoma is a rare subtype of cutaneous lymphomas with distinct clinical, histological and immunophenotypic characteristics, as well as an indolent clinical course. Rarely, it may be complicated with hemophagocytic lymphohistiocytosis: a hyperinflammatory syndrome which, if not diagnosed early, carries a dismal outcome. In this article, we describe a case of subcutaneous panniculitis-like T cell lymphoma in a middle-aged female patient which was complicated with secondary hemophagocytic lymphohistiocytosis with a favorable outcome following etoposide-based therapy. The various histological mimics of subcutaneous panniculitis-like T cell lymphoma and the management options are also briefly discussed.


How to cite this article:
Sirka CS, Pradhan S, Patra S, Padhi S, DasMajumdar SK, Panda D. Hemophagocytic lymphohistiocytosis: A rare, potentially fatal complication in subcutaneous panniculitis like T cell lymphoma.Indian J Dermatol Venereol Leprol 2019;85:481-485


How to cite this URL:
Sirka CS, Pradhan S, Patra S, Padhi S, DasMajumdar SK, Panda D. Hemophagocytic lymphohistiocytosis: A rare, potentially fatal complication in subcutaneous panniculitis like T cell lymphoma. Indian J Dermatol Venereol Leprol [serial online] 2019 [cited 2020 Sep 22 ];85:481-485
Available from: http://www.ijdvl.com/article.asp?issn=0378-6323;year=2019;volume=85;issue=5;spage=481;epage=485;aulast=Sirka;type=0


 

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