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 Table of Contents    
IMAGES IN CLINICAL PRACTICE
Year : 2017  |  Volume : 83  |  Issue : 6  |  Page : 728-729

Pseudoainhum and autoamputation associated with lamellar ichthyosis


1 Department of Dermatology, Venereology and Leprology, JIPMER, Puducherry, India
2 Department of Pathology, JIPMER, Puducherry, India

Date of Web Publication21-Sep-2017

Correspondence Address:
Devinder Mohan Thappa
Department of Dermatology, Venereology and Leprology, JIPMER, Puducherry - 605 006
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/ijdvl.IJDVL_56_17

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How to cite this article:
Behera B, Gochhait D, Thappa DM. Pseudoainhum and autoamputation associated with lamellar ichthyosis. Indian J Dermatol Venereol Leprol 2017;83:728-9

How to cite this URL:
Behera B, Gochhait D, Thappa DM. Pseudoainhum and autoamputation associated with lamellar ichthyosis. Indian J Dermatol Venereol Leprol [serial online] 2017 [cited 2020 Jul 12];83:728-9. Available from: http://www.ijdvl.com/text.asp?2017/83/6/728/215286


A 6-month-old female child born out of first-degree consanguineous marriage was brought by the parents with complaints of scaling all over the body since birth. The parents gave a positive history of collodion membrane at birth which gradually peeled off after 1 month of life. Cutaneous examination revealed large thick brown-colored adherent plate-like scales all over the body, ectropion, contracture of fingers, and palmoplantar keratoderma without eclabium. Bilateral fingers and toes showed multiple partial constriction bands around them; a feature suggestive of pseudoainhum [Figure 1] and [Figure 2]. The tip of the right middle finger was autoamputated [Figure 1]. The nail plates of few nails were completely replaced by hyperkeratotic scales. Skin biopsy showed marked compact hyperkeratosis with a normal granular layer, mild-to-moderate acanthosis, and mild perivascular lymphocytic infiltration. A diagnosis of lamellar ichthyosis was made and the child was started on capsule acitretin 1 mg/kg/day orally.
Figure 1: Multiple constriction bands over the right-hand fingers (arrows) and autoamputation of the tip of right middle finger

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Figure 2: Multiple constriction bands over the left feet toes (arrows)

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Financial support and sponsorship

Nil.

Conflflicts of interest

There are no conflicts of interest.


    Figures

  [Figure 1], [Figure 2]



 

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