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Year : 2012  |  Volume : 78  |  Issue : 3  |  Page : 407-

Congenital self-healing histiocytosis presenting as blueberry muffin baby: A case report and literature review


1 Clinic of Dermatovenereology, Clinical Center of Serbia, Department of Dermatovenereology, Faculty of Medicine, University of Belgrade, Belgrade, Serbia
2 Institute of Pathology, Faculty of Medicine, University of Belgrade, Belgrade, Serbia

Correspondence Address:
Milos Nikolic
Clinic of Dermatovenereology, Faculty of Medicine, University of Belgrade, Pasterova 2, 11000 Belgrade
Serbia
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/0378-6323.95482

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Congenital self-healing Langerhans cell histiocytosis (CSHLCH), also called as Hashimoto-Pritzker disease, is a rare, benign variant of histiocytosis. Despite the initial dramatic clinical presentation, affected infants are otherwise healthy and skin lesions disappear spontaneously within several weeks to months. We present a case of CSHLCH presenting as blueberry muffin baby. The lesions appeared in the first week of life and lasted 6 months. The follow-up period was 24 months, without any signs of relapse. At the pediatric dermatology unit of our clinic, during the last 20 years, we had 10 children with Langerhans cell histiocytosis and among them only one with CSHLCH. In the literature, we found only 5 newborns with Langerhans cell histiocytosis presenting as blueberry muffin baby, among them only 4 with self-healing CSHLCH. The early recognition of CSHLCH may spare children from redundant and potentially toxic systemic treatment.






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Online since 15th March '04
Published by Wolters Kluwer - Medknow