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LETTER TO EDITOR
Year : 1995  |  Volume : 61  |  Issue : 4  |  Page : 242-243

Connective tissue naevus-naevus elasticus




Correspondence Address:
Mohan Devinder Thappa


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Source of Support: None, Conflict of Interest: None


PMID: 20952976

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How to cite this article:
Thappa MD, Garg B R, Ratnakar C. Connective tissue naevus-naevus elasticus. Indian J Dermatol Venereol Leprol 1995;61:242-3

How to cite this URL:
Thappa MD, Garg B R, Ratnakar C. Connective tissue naevus-naevus elasticus. Indian J Dermatol Venereol Leprol [serial online] 1995 [cited 2019 Sep 21];61:242-3. Available from: http://www.ijdvl.com/text.asp?1995/61/4/242/4229



  To the Editor, Top


Juvenile elastoma (naevus elasticus) is a connective tissue naevus of elastin that may occur as a sporadic isoloated lesion or multiple lesions as the Buschke-Ollendorf syndrome.[1],[2] We, herewith, report a case of juvenile elastoma in a 21-year-old male for its rarity and clinical interest.

A 21-year-old male noticed an asymptomatic gradually increasing swelling over the midline of back for last 5 years. There was no history of seizures. No family history of similar lesions was forthcoming. Cutaneous examination revealed a single, oval, soft to firm, 3x4 cm subcutaneous swelling with dermal infiltration at T12 level in the midline back. Overlying skin, which had an "orange peel" appearance, was topped by 2 to 3mm sized soft papular lesions numbering five in total and a 5 mm sized hyperpigmented, raised soft nodule having furrowed skin. No ash leaf macules, adenoma sebaceum, cafe-au-lait macules or neurofibromas were seen. Rest of cutaneous and systemic examination was unremarkable. Routine laboratory examination was within normal limits. Skiagram of dorsolumbar spine did not show any abnormality. Microscopic examination of the lesions showed mild hyperkeratosis in the epidermis. The reticular dermis showed collagenisation. Verhoff-Von Gieson stain showed marked increase in the elastic fibres but there was no evidence of degeneration of elastic fibres.

The term naevus elasticus was first used by Lewandowsky[3] under the title of "Naevus Elasticus Regionis Mammariae" to describe a condition appearing in the pectoral regions and being characterised by groups of perifollicular papules which histologically showed disappearance and degeneration of the elastic fibres. Staricco and Mehregan,[2] however, later emphasized the use of the term naevus elasticus for a localised naevoid disturbance of elastic fibres, characterised by pure excess of normal appearing fibres. The use of term naevus anelasticus for Lewandowsky's naevus was justified. The naevus elasticus has been described under a variety of names such as dystrophia elastica follicularis thoracica, naevus pseudocolloid perifolliculaire, naevus conjunctivus and juvenile elastoma.[2] It is generally found in young children and is characterised by skin coloured or white-yellowish tumours varying in size from few mm to one centimeter, isolated or grouped in plaques, generally distributed on the back, the lumbar regions, the abdomen and thighs.[2] The features observed in our case were compatible with sporadic isolated form.

These connective tissue naevi are subtle at birth and may go unnoticed. They tend to persist throughout the life. Clinically, the appearance is so characterisitic that they are seldom misdiagnosed.

 
  References Top

1.Verbov J, Graham R. Buschke-Olendorf syndrome-disseminated dermatofibrosis with osteopoikilosis. Clin Exp Dermatol 1986;11:17-26.  Back to cited text no. 1  [PUBMED]  
2.Staricco RG, Mehregan AH. Nevus elasticus and nevus elasticus vascularis. Arch Dermatol 1961;84:105-9.  Back to cited text no. 2  [PUBMED]  
3.Lewandowsky F. Naevus elasticus regionis mammariae. Arch Clin Exp Derm 1921;90:131.  Back to cited text no. 3    




 

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