|Year : 1991 | Volume
| Issue : 3 | Page : 150-151
Vijay Kumar, RB Garg, CM Baruah, C Ratnakar
Source of Support: None, Conflict of Interest: None
A 10-year-old girl having syringocystadenoma papilliferum lesions on back is described. The entire lesions were excised and skin grafting was done.
Keywords: Syringocystadenoma papilliferum
|How to cite this article:|
Kumar V, Garg R B, Baruah C M, Ratnakar C. Syringocystadenoma papilliferum. Indian J Dermatol Venereol Leprol 1991;57:150-1
|How to cite this URL:|
Kumar V, Garg R B, Baruah C M, Ratnakar C. Syringocystadenoma papilliferum. Indian J Dermatol Venereol Leprol [serial online] 1991 [cited 2019 Sep 17];57:150-1. Available from: http://www.ijdvl.com/text.asp?1991/57/3/150/3655
Syringocystadenoma papilliferum is a be要ign tumor of the epidermal appendages of disputed origin. The fact that 90% of all le貞ions occur on body surface where apocrine glands normally do not occur, favours an ec苞rine derivation theory of Helwig and Hack要ey. While according to Pinkus, the most lesions of syringocystadenoma papilliferum are apocrine and some are eccrine in differentia負ion. We report a case of syringocystadenoma papilliferum with multiple lesions at the back which has not been reported so far.
| Case Report|| |
A 10-year-old girl came to our hospital with asymptomatic, multiple, small swellings on her back since birth. The lesions were slowly increasing in size and some occasion苔lly used to bleed on minor trauma. There was no family history of similar lesions.
On examination, a group of multiple papules and nodules [Figure - 1] of varying sizes ranging from 1 mm to 20 mm in diameter were present over lower back. Most of the lesions were skin coloured and others had pinkish hue. The bigger lesions were covered with crust. All the lesions were soft to firm in consistency but only some lesions were com計ressible. Some lesions bled on scratching. There was no significant lymphadenopathy and systemic examination did not reveal any abnormality.
All the routine investigations including haemogram, urine, stool and liver function tests were normal. Histopathological exami要ation of one of the lesions revealed a clas貞ical histopathology of syringocystadenoma papilliferum [Figure - 2].
The entire lesions were excised and skin grafting was done.
| Comments|| |
In our patient the lesions were present on the back since birth having history of bleeding on trauma, which were compressible and crusted, hence the diagnosis of angiokeratoma circumscripta was thought clinically. After histopathological examination only a diagnosis of syringocystadenoma papilliferum was made. Syringocystadenoma papilliferum usually presented on the scalp or over the face but it can be seen elsewhere.,, Papules in a linear arrangement over left arm and segmental distribution across the left side of the chests have been described. Helwig and Hackney described 7 patients with soli負ary lesions at back, whereas in our case there were multiple lesions arranged in a group at the back.
| References|| |
|1.||Lever WF and Gundula SL : Syringocystadenoma papilliferum, in : Histopathology of the skin, 6th ed, Editors, pedersen DD : JB Lippincott, Philadel計hia,1983; p 544-546. |
|2.||Pinkus H : Life history of naevus syringadenomatous papilliferous, Arch Dermatol Syphilol, 1954; 63 : 305-322. |
|3.||Helwig EB and Hackney C : Syringadenoma papilliferum, Arch Dermatol, 1955; 71 : 361-372. |
|4.||Rostan SE and Waller JD : Syringocystadenoma papilliferum in an unusual location, Arch Dermatol, 1976; 112 : 835-836. |
|5.||Premalatha S, Rao NR, Yesudian P et al : Seg衫ental syringocystadenoma papilliferum in an unusual location, Internat J Dermatol, 1985; 24 520-521. |
[Figure - 1], [Figure - 2]